Congenital self-healing reticulohistiocytosis

(Redirected from Hashimoto-Pritzker disease)

Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]: 720 

Congenital self-healing reticulohistiocytosis
Other namesHashimoto–Pritzker disease,[1] and Hashimoto–Pritzker syndrome[2]
SpecialtyDermatology

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]

Diagnosis

Treatment

History

It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.[4][5]

See also

References